Polimiositis-dermatomiositis y embarazo

Claudino Molinero Rodríguez, Dinorah Marisabel Prada Hernández, Jorge Alexis Gómez Morejón, Mara Victoria Hernández Cuellar, Isabel María Hernández Cuellar, Joel Milera Rodríguez, Janet Rodríguez Zulueta, Ana Marta López Mantecón, Yusimí Reyes Pineda, Jany Gil Prada, Jorge López Valdés, Anabel Rodríguez Rodríguez

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Resumen

La polimiositis-dermatomiositis  es una enfermedad  inflamatoria  difusa del músculo estriado, de causa desconocida, existiendo actualmente evidencias de la participación de  factores inmunológicos en su patogenia, En cuanto a su frecuencia, pueden considerarse dentro del grupo de enfermedades raras debido a su baja incidencia, la afectación principal es a nivel de piel y músculos, con las variantes de ser un proceso agudo, sub- agudo y crónico,  pudiendo ocasionar atrofia y degeneración muscular. Las miopatías inflamatorias idiopáticas son entidades diferenciadas, tanto desde el punto de vista etiopatogénicos como terapéutico y pronóstico. Sin embargo, a la hora de publicar las diferentes experiencias con pacientes embarazadas no se hacen grandes diferencias entre polimiositis y dermatomiositis. Los reportes de polimiositis-dermatomiositis y embarazo son infrecuentes debido probablemente a que la enfermedad no es habitual y que el pico de la presentación más frecuente se encuentre alrededor de los 50 años.

Palabras clave

polimiositis y embarazo; dermatomiositis y embarazo

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