Idiopathic dermatomyositis associated with pulmonary fibrosis
Keywords:
dermatomyositis, pulmonary fibrosisAbstract
The incidence of Idiopathic Inflammatory Myopathy is from 4 to 15 cases per million inhabitants and its prevalence of 60 per million inhabitants. Idiopathic dermatomyositis is more frequent in women; Although its association with pulmonary fibrosis is described, it is very infrequent, it is only reported in 2% of cases. To describe a diagnosed case of idiopathic dermatomyositis and pulmonary fibrosis. A 50-year-old patient presented weakness at the level of the shoulder girdle accompanied by fatigue. Physical examination: Skin: scratching lesions in different regions of the body due to pruritus, erythematous lesions at the level of the skin on both thighs. Osteomyoarticular system: generalized joint pains with functional impotence and progressive generalized myalgias and muscular hypotrophy of several muscle groups. The analytical study revealed elevated muscle enzymes. The skin and muscle biopsy showed elements suggestive of dermatomyositis. Chest X-ray: diffuse peribronchovascular infiltrate associated with fibrous path. Spirometry: restrictive ventilatory disorders of severe intensity. Computed tomography of the lung with alveolar consolidation and discrete pleural thickening. We report the case of a patient with idiopathic dermatomyositis and pulmonary fibrosis. This association is an uncommon finding in our environment and even more so when the patient is asymptomatic.Downloads
References
Arnaud L, Amoura Z. Criterios de clasificación de las conectivopatías. EMC Tratado de Medicina. 2012; 16(3):1-5
Bohan A, Peter J. Polymyositis and Dermatomyositis. New Eng J Med, 1975, 292: 344-403.
Turrión Nieves AL, Martín Holguera R, Sánchez Atrio AL, Moruno Cruz H. Miopatías inflamatorias idiopáticas. Medicina 2013; 11(33):2040‒7.
Miller F. Polimiositis y Dermatomiositis. En Principios de Medicina Interna. Cecil Goldman (eds). Edición 24, Edit Elsevier, Madrid 2013, p 1720- 5.
Lazarou IN, Guerme FA. Classification, diagnosis and management of idiopathic inflammatory myopathies. J Rheumatol. 2013;40 (5):550‒64.
J. Svensson, E.V. Arkema, I.E. Lundberg, M. Holmqvist.Incidence and prevalence of idiopathic inflammatory myopathies in Sweden: a nationwide population-based study.Rheumatology (Oxford). 56 (2017 May 1), pp. 802-810 http://dx.doi.org/10.1093/rheumatology/kew503
Russi J, Paz A, Valdes J, Rodríguez D, ValenciaJ, Mona G. Polimiositis y compromiso cardíaco. Acta Med Colom 2014; 39:293-297.
I.E. Lundberg, M. de Visser, V.P. Werth. Classification of myositis. Nat Rev Rheumatol., 14 (2018 May), pp. 269-27 http://dx.doi.org/10.1038/nrrheum.2018.41
Miller M, Vleugels R. Clinical manifestations of Dermatomyosytis and Polymyositis in adults. Up to date, 2013.
N.J. McHugh, S.L. Tansley. Autoantibodies in myositis. Nat Rev Rheumatol., 14 (2018 Apr 20), pp. 290-302 http://dx.doi.org/10.1038/nrrheum.2018.56
Bouza Jiménez Y; Núñez Paredes I M; Perez Rodríguez Y et al. Dermatomiositis. Presentación de un caso: Case presentation. Medisur [online]. 2018, vol.16, n.2, pp.335-343. ISSN 1727-897X.
I.E. Lundberg, A. Tjärnlund, M. Bottai, et al. European League Against Rheumatism/American College of Rheumatology classification criteria for adult and juvenile idiopathic inflammatory myopathies and their major subgroups. Ann Rheum Dis., 76 (2017 Dec), pp. 1955-1964 http://dx.doi.org/10.1136/annrheumdis-2017-211468
Downloads
Published
How to Cite
Issue
Section
License
Warning of rights of author
The authors that publish in this journal agree with the following terms:
The authors conserve the rights of author and concede to the journal the right of the first publication, fulfilling with the license Creative Commons Attribution License that allows to others share the work with recognition of the authorship of their articles, and the initial publication in this journal.
The authors can establish separately additional agreements for the no exclusive distribution of the version of the work published in the journal (for example, situate it in an institutional repository, in a personal blog or publish it partial or totally in a book), with a recognition of their initial publication in this journal.
To be able to send the manuscript or part of him passed three months of published, for his evaluation to other publishers, identifying it or not with the same title; whenever allusion is made to our journale and know it the new publisher.
The publishing committee of the Cuban Journal of Rheumatology authorizes to other publishers, to reproduce the articles published in our magazine, whenever it indicate the origin of the same.
The authors should send a document in Office Word application format through the electronic address of the magazine with a similar format to that we include next:
---------------------------------------------------------------------------------------------------------------------
Statement of authorship and cede of articles for the publication of the scientific work in the Cuban Journal of Rheumatology
Date:
Those who subscribe certify that are the authors of the work:
Of this form communicate the originality of our article clearing that the concepts and knowledges of other authors that have included in the text of the article, have been quoted properly in the bibliography.
We do proof besides that the article in question is original and has not been published, total neither partially, in another journal.
To be approved for his publication in the Cuban Journal of Rheumatology, do secession of the rights of publication to the same one through the method that realizes it usually.
In front of any catchword that exist by the article that send to evaluate, relieve of of the responsibility to the Cuban Journal of Rheumatology holding us responsible with all the difficulties that can berelated by any situation.
We include to continuation the name and the signature of all authors and collaborators of this article.
Name: Signature:
