Cava vein syndrome in patient with Behçet's disease

Authors

  • Lina Maria Saldarriaga Rivera Departamento de Reumatología. Hospital Universitario Clementino Fraga Filho. Universidad Federal de Rio de Janeiro, Brasil
  • Guilherme da Silveira Campos Departamento de Reumatología. Hospital Universitario Clementino Fraga Filho. Universidad Federal de Rio de Janeiro, Brasil
  • Luis Alberto Delgado Quiroz Departamento de Reumatología. Hospital Universitario Clementino Fraga Filho. Universidad Federal de Rio de Janeiro, Brasil
  • Blanca Elena Rios Gomes Bica Departamento de Reumatología. Hospital Universitario Clementino Fraga Filho. Universidad Federal de Rio de Janeiro, Brasil

Keywords:

thrombosis, Behçet's disease, latent tuberculosis, Cava vein

Abstract

Behçet's disease includes a set of clinical manifestations characterized by the presence of recurrent oral ulcers, multiple painful genital ulcers associated with eye involvement, skin and vascular lesions. We describe a patient with Behçet's disease presenting thrombosis of the superior Cava vein.

Downloads

Download data is not yet available.

Author Biographies

Lina Maria Saldarriaga Rivera, Departamento de Reumatología. Hospital Universitario Clementino Fraga Filho. Universidad Federal de Rio de Janeiro, Brasil

Especialista en Medicina Interna. Residente de 2do año de Reumatología

Guilherme da Silveira Campos, Departamento de Reumatología. Hospital Universitario Clementino Fraga Filho. Universidad Federal de Rio de Janeiro, Brasil

Especialista en Medicina Interna. Residente de 2do año de Reumatología

Luis Alberto Delgado Quiroz, Departamento de Reumatología. Hospital Universitario Clementino Fraga Filho. Universidad Federal de Rio de Janeiro, Brasil

MSc. Especialista en Reumatología, Alergia e Inmunología

Blanca Elena Rios Gomes Bica, Departamento de Reumatología. Hospital Universitario Clementino Fraga Filho. Universidad Federal de Rio de Janeiro, Brasil

MSc. PhD. Especialista en Reumatología Pediátrica

References

Jennette1 JC, Falk RJ, Bacon PA, Basu N, Cid MC, Ferrario F, Flores-Suarez LF, et al. Revised International Chapel Hill Consensus Conference Nomenclature of Vasculitides. Arthritis & Rheumatism. 2013;65(1):1-11.

Wurmann P, Díaz G, Sabugo F, Soto L, Solanes F, Pino S, Cuchacovich M. Enfermedad de Behçet en Chile:Análisis clínico de 44 casos. Rev méd Chile. 2009;137(10):1333-40.

Mutlu S, Scully C. The person behind the eponym: Hulûsi Behcet (1889‐1948). Journal of oral pathology & medicine. 1994;23(7):289-90.

International Team for the Revisin of the Internacional Criteria for Behçet's Disease (ITR-ICBD). Revision of the International Criteria for Behçet's Disease (ICBD). Clin Exp Rheumatol. 2006;24 suppl 42:14-5.

Yurdakul S, Hamuryudan V, Yazici H. Behçet syndrome. Current opinion in rheumatology. 2004;16(1):38-42.

Seyahi E, Melikoglu M, Yazici H. Clinical features and diagnosis of Behcet's syndrome. Int J Adv Rheumatol. 2007;5(1):8-11.

De_Souza Neves F, Bertacini de_Moraes JC, Gonçalves CR. Síndrome de Behçet: ? procura de evidencias. Rev Bras Reumatol. 2006;1:7-10.

Diri E, Mat C, Hamuryudan V, Yurdakul S, Hızlı N. Papulopustular skin lesions are seen more frequently in patients with Behçet's syndrome who have arthritis: a controlled and masked study. Annals of the rheumatic diseases. 2001;60(11):1074-76.

Tugal-Tutkun I, Onal S, Altan-Yaycioglu R, Huseyin Altunbas H, Urgancioglu M.. Uveitis in Behçet disease: an analysis of 880 patients. Am J Ophthalmol. 2004;138(3):373-78.

Lie JT. (Vascular involvement in Behçet's disease: arterial and venous and vessels of all sizes. Journal of rheumatology. 1992;19(3):341-3.

Sarica-Kucukoglu R, Akdag-Kose A, Kayabal IM, Yazganoglu KD, Disci R, Erzengin D, et-al. Vascular involvement in Behçet's disease: a retrospective analysis of 2319 cases. Int J Dermatol. 2006;45:919.

Fessler Bj. Thrombotic syndromes and autoimmune diseases. Rheuma Dis Clin North Am. 1997;23:461-70.

Published

2014-05-21

How to Cite

1.
Saldarriaga Rivera LM, da Silveira Campos G, Delgado Quiroz LA, Rios Gomes Bica BE. Cava vein syndrome in patient with Behçet’s disease. Rev. cuba. de Reumatol. [Internet]. 2014 May 21 [cited 2025 Mar. 14];16(2):230-4. Available from: https://revreumatologia.sld.cu/index.php/reumatologia/article/view/283

Issue

Section

Studies of cases