Chronic Recurrent Multifocal Osteomyelitis: presentation of case

Authors

  • Ariel Moya Machado Universidad Médica de Villa Clara Dr. Serafín Ruiz de Zarate Ruiz. Hospital Pediátrico Universitario José Luis Miranda. Santa Clara. Villa Clara.
  • Margarita Hernández Garcia Universidad Médica de Villa Clara Dr. Serafín Ruiz de Zarate Ruiz. Hospital Pediátrico Universitario José Luis Miranda. Santa Clara. Villa Clara.
  • Leidelen Esquivel Sosa Universidad Médica de Villa Clara Dr. Serafín Ruiz de Zarate Ruiz. Hospital Pediátrico Universitario José Luis Miranda. Santa Clara. Villa Clara.

Keywords:

chronic recurrent multifocal osteomyelitis, CRMO, autoinflammatory disease, multiple osteolytic lesions

Abstract

Autoinflammatory syndromes are a group of diseases characterized by spontaneous, recurrent or persistent episodes of multisystem inflammation. They do not show an infectious, neoplastic or autoimmune etiology. They are caused by alterations of the innate immunity, which causes a dysregulation of the inflammatory system at the level of the inflammasome. These syndromes are subdivided into two major groups, the hereditary syndromes of periodic fever and the persistent autoinflammatory diseases; within the latter are the inflammatory bone diseases which chronic recurrent multifocal osteomyelitis. We present a case of a 9-year-old girl who enters our hospital due to a prolonged febrile syndrome and after multiple investigations, it concludes as a Chronic Recurrent Multifocal Osteomyelitis.

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Author Biographies

Ariel Moya Machado, Universidad Médica de Villa Clara Dr. Serafín Ruiz de Zarate Ruiz. Hospital Pediátrico Universitario José Luis Miranda. Santa Clara. Villa Clara.

MSc. Especialista de 2do Grado en Pediatría.

Margarita Hernández Garcia, Universidad Médica de Villa Clara Dr. Serafín Ruiz de Zarate Ruiz. Hospital Pediátrico Universitario José Luis Miranda. Santa Clara. Villa Clara.

MSc. Especialista de 1er Grado en Reumatología.

Leidelen Esquivel Sosa, Universidad Médica de Villa Clara Dr. Serafín Ruiz de Zarate Ruiz. Hospital Pediátrico Universitario José Luis Miranda. Santa Clara. Villa Clara.

Especialista de 1er Grado en Medicina General Integral e Imagenología.

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Published

2018-01-31

How to Cite

1.
Moya Machado A, Hernández Garcia M, Esquivel Sosa L. Chronic Recurrent Multifocal Osteomyelitis: presentation of case. Rev. cuba. de Reumatol. [Internet]. 2018 Jan. 31 [cited 2025 Dec. 6];20(1):e08. Available from: https://revreumatologia.sld.cu/index.php/reumatologia/article/view/589

Issue

Section

Studies of cases