Wegener's granulomatosis, a rare condition
DOI:
https://doi.org/10.5281/zenodo.2555184Keywords:
quality of life, Wegener's granulomatosis, systemic vasculitisAbstract
Introduction: Wegener's granulomatosis is a rare systemic vasculitis, whose etiopathogenic substrate is the inflammation of the blood vessels, preventing the free circulation of blood flow. Clinically it is characterized by the presence of respiratory, nasal, auditory and renal manifestations; Infectious and allergic disorders are frequently associated.
Objective: to socialize the main etiopathogenic elements, clinical manifestations and complementary examinations that allow us to define Wegener's granulomatosis.
Clinical case: the case of a 32-year-old female patient is reported from primary health care, due to clinical and laboratory manifestations that confirm the diagnosis of Wegener's granulomatosis.
Conclusions: Wegener's granulomatosis is a rare disease that, although it occurs mainly in female patients between 40 and 50 years, can occur in patients of any age without distinguishing preference for sex. Its main clinical manifestations are respiratory and renal uptake accompanied by general manifestations. The use of steroids is the cornerstone of the treatment, to which are added medications for the control of the disease such as methotrexate.
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