Neumonía intersticial con características autoinmunes: reporte de caso

Authors

  • Andres Usma Universidad Tecnológica de Pereira, Facultad de Medicina, Grupo de Investigación en Medicina Interna. Pereira, Risaralda https://orcid.org/0000-0001-5315-1943
  • Valentina Prieto Universidad Tecnológica de Pereira, Facultad de Medicina, Grupo de Investigación en Medicina Interna. Pereira, Risaralda https://orcid.org/0000-0002-8997-9715
  • Darwin Zambrano Universidad Tecnológica de Pereira, Facultad de Medicina, Grupo de Investigación en Medicina Interna. Pereira, Risaralda https://orcid.org/0000-0002-8774-5173
  • Christian Marin Giraldo Universidad Tecnológica de Pereira, Facultad de Medicina, Grupo de Investigación en Medicina Interna. Pereira, Risaralda https://orcid.org/0000-0002-0511-7350
  • Angela Maria Giraldo Montoya Universidad Tecnológica de Pereira, Facultad de Medicina, Grupo de Investigación en Medicina Interna. Pereira, Risaralda. Clínica los Rosales, Servicio de Neumología. Pereira, Risaralda https://orcid.org/0000-0003-1310-3714
  • Lina Maria Saldarriaga Rivera Departamento de Reumatología. Hospital Universitario Clementino Fraga Filho. Universidad Federal de Rio de Janeiro, Rio de Janeiro. Universidad Tecnológica de Pereira, Facultad de Medicina, Grupo de Investigación en Medicina Interna. Pereira, Risaralda Clínica los Rosales, Servicio de Reumatología. Pereira, Risaralda https://orcid.org/0000-0001-5180-367X

Keywords:

enfermedades pulmonares, neumonía intersticial, fibrosis pulmonar idiopática, enfermedades del tejido conectivo.

Abstract

La neumonía intersticial con características autoinmunes por sus siglas en inglés, es una entidad en la que existe un compromiso pulmonar intersticial y hallazgos clínicos y paraclínicos que sugieren una enfermedad del tejido conectivo, pero sin lograr cumplir criterios diagnósticos para ninguna de estas. Con fines de investigación, se describieron en 2015 criterios para esta entidad, en los que se incluyen características de dominios clínicos, serológicos y morfológicos, con diversos patrones de compromiso pulmonar. En la actualidad hay un aumento en el interés de esta entidad, pues algunos autores sugieren que se pueda tratar de una patología autoinmune per se, cuyo órgano blanco principal sería el pulmón. Dado su reciente reconocimiento, son pocos los casos descritos en la literatura y por lo tanto con fines de contribuir a la mejor identificación de esa entidad, presentamos el caso de una paciente de 65 años con afectación pulmonar en quien después de descartar otras causas etiológicas se llegó al diagnóstico de neumonía intersticial con características autoinmunes al cumplir criterios de cada dominio requerido.

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Author Biography

Lina Maria Saldarriaga Rivera, Departamento de Reumatología. Hospital Universitario Clementino Fraga Filho. Universidad Federal de Rio de Janeiro, Rio de Janeiro. Universidad Tecnológica de Pereira, Facultad de Medicina, Grupo de Investigación en Medicina Interna. Pereira, Risaralda Clínica los Rosales, Servicio de Reumatología. Pereira, Risaralda

Especialista en Medicina Interna

Especialista en Reumatología

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Published

2020-07-18

How to Cite

1.
Usma A, Prieto V, Zambrano D, Marin Giraldo C, Giraldo Montoya AM, Saldarriaga Rivera LM. Neumonía intersticial con características autoinmunes: reporte de caso. Rev. cuba. de Reumatol. [Internet]. 2020 Jul. 18 [cited 2025 Apr. 4];22(3):e159. Available from: https://revreumatologia.sld.cu/index.php/reumatologia/article/view/795

Issue

Vol. 22 No. 3 (2020): Julio-Septiembre

Section

Studies of cases

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