Undifferentiated connective tissue disease associated with deficiency of IgG2 and IgG4

Authors

  • Lina María Saldarriaga Rivera Servicio de Reumatología del Hospital Universitario Clementino Fraga Filho. Universidad Federal de Rio de Janeiro, Brasil (HUCFF-UFRJ)L
  • Luis Alberto Delgado Quiroz Servicio de Reumatología del Hospital Universitario Clementino Fraga Filho. Universidad Federal de Rio de Janeiro, Brasil (HUCFF-UFRJ)
  • Blanca Elena Ríos Gomes Bica Servicio de Reumatología del Hospital Universitario Clementino Fraga Filho. Universidad Federal de Rio de Janeiro, Brasil (HUCFF-UFRJ)

Keywords:

connective tissue disease, IgG deficiency, autoimmune disease, immunodeficiency

Abstract

The undifferentiated connective tissue disease is a condition of unknown etiology that shares clinical, pathological and laboratory characteristics with several collagenosis, without meeting the criteria of the American College of Rheumatology (ACR) for the diagnosis of a specific rheumatic disease. The IgG subclass deficiency term refers to a significant decrease in serum concentrations of one or more IgG subclasses in a patient whose total IgG concentration is normal, presenting recurrent bronchitis, sinusitis or otitis. We report the case of a female patient diagnosed with undifferentiated connective tissue disease associated with deficiency of IgG2 and IgG4.

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Author Biographies

Lina María Saldarriaga Rivera, Servicio de Reumatología del Hospital Universitario Clementino Fraga Filho. Universidad Federal de Rio de Janeiro, Brasil (HUCFF-UFRJ)L

Especialista en Medicina Interna. Residente de segundo año de Reumatología

Luis Alberto Delgado Quiroz, Servicio de Reumatología del Hospital Universitario Clementino Fraga Filho. Universidad Federal de Rio de Janeiro, Brasil (HUCFF-UFRJ)

MSc. Especialista en Reumatología, Alergia e Inmunología

Blanca Elena Ríos Gomes Bica, Servicio de Reumatología del Hospital Universitario Clementino Fraga Filho. Universidad Federal de Rio de Janeiro, Brasil (HUCFF-UFRJ)

MSc, PhD. Especialista en Reumatología Pediátrica

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Enfermedad Indiferenciada del Tejido Conectivo asociada a deficiencia de IgG2 e IgG4

Published

2014-04-01

How to Cite

1.
Saldarriaga Rivera LM, Delgado Quiroz LA, Ríos Gomes Bica BE. Undifferentiated connective tissue disease associated with deficiency of IgG2 and IgG4. Rev. cuba. de Reumatol. [Internet]. 2014 Apr. 1 [cited 2025 Feb. 7];16(1):47-51. Available from: https://revreumatologia.sld.cu/index.php/reumatologia/article/view/297

Issue

Section

Studies of cases

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